AUTOCRINE ROLE OF FGF2 IN VASCULAR TUMORS

Blood vessels may represent the site of origin for neoplasms, hamartomas, and vessel malformations. Neoplasms include benign tumors and tumor-like lesions (hemangioma), tumors of intermediate malignancy (hemangioendothelioma), and malignant tumors (angiosarcoma) (Enzinger, 1995). The pathogenesis of vascular tumors is at present unknown, even though the local, uncontrolled release of growth factors and/or lytic enzymes has been hypothesized to facilitate endothelial cell proliferation and the formation of vascular lacunae (Enzinger, 1995).

           Benign vascular tumor



A close relationship exists between the formation of vascular tumors and angiogenesis. This relationship is also apparent in Kaposi's sarcoma (KS). Classic KS is a relatively benign, highly vascularized neoplasm. A clinically aggressive form of KS develops in a significant percentage of acquired immune deficiency syndrome (AIDS) patients (Levine, 1993). Histologically, KS is characterized by the presence of spindle-shaped cells, inflammatory cells and newly formed blood vessels (Enzinger, 1995). KS lesions express various markers for vascular endothelial cells, suggesting that KS spindle cells are of endothelial cell lineage (Sturzl et al., 1992).

Kaposi sarcoma



Several experimental evidences implicate FGF2 in the pathogenesis of vascular lesions, including KS and hemangiomas. In vitro, AIDS-KS cells derived from different patients express high levels of FGF2 which is released in the extracellular media (Albini et al., 1994). Antisense oligonucleotides directed against FGF2 mRNA inhibit both the growth of AIDS-KS cells and the angiogenic activity associated with these cells, including the induction of KS-like lesions in nude mice (Ensoli et al., 1994b). FGF2 immunoreactivity is detected both in classic and AIDS-associated KS lesions in humans (Ensoli et al., 1994a) and recombinant FGF2 synergizes with HIV-1-Tat protein in inducing the formation of vascular lesions closely resembling early KS into nude mice (Ensoli et al., 1994).

Interestingly, cytokines from activated T cells induce FGF2 upregulation and the acquisition of a AIDS-KS spindle cell-like phenotype in normal endothelial cells (Barillari et al., 1992; Fiorelli et al., 1995). Finally, coexpression of FGF2 and endothelial phenotypic markers CD31 and von Willebrand factor has been found in the proliferating phase of human hemangioma but not in vascular malformations (Takahashi et al., 1994). Taken together, the data suggest that FGF2 produced by cells of the endothelial lineage may play important autocrine and paracrine roles in the pathogenesis of vascular tumors.